Protein Name:
Probable methylcrotonoyl-CoA carboxylase beta chain, mitochondrial
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UniprotKB/SwissProt ID: Q9V9A7 (Q9V9A7)
Gene Name:
Mccc2
Organism: Drosophila melanogaster (Fruit fly)
Function: Carboxyltransferase subunit of the 3-methylcrotonyl-CoA carboxylase, an enzyme that catalyzes the conversion of 3-methylcrotonyl-CoA to 3-methylglutaconyl-CoA, a critical step for leucine and isovaleric acid catabolism (By similarity). Vital for adult survival
Other Modifications: View all modification sites in dbPTM
Protein Subcellular Localization: Mitochondrion matrix
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Graphical Visualization of S-nitrosylation Sites:
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